Focal Fibrocartilaginous Dysplasia in Distal Radius

نویسندگان

  • Farid Najd Mazhar
  • Hooman Shariatzadeh
  • Ali Dianat
  • Davod Jafari
چکیده

Background: Focal fibrocartilaginous dysplasia (FFCD) is a benign lesion and has been reported as a cause of tibia vara in proximal tibia and distal of the femur. It is rare in upper extremity and few cases have been reported in the ulna and radius. Objectives: The aim of the study was to review and report the clinical course, radiographic presentation and treatment results of three cases of FFCD in the distal radius. Patients and Methods: We reviewed the medical records, imaging files, intraoperative anatomical findings and treatment complications of three cases of FFCD in distal radius. All patients underwent tethering fibrotic band resection with lengthening of extensor tendons in one case and distal radius corrective osteotomy in another one. Results: All three patients were male with a mean age of 21.3 (11 36) months. The mean follow-up period was 28 months. Clinical and radiographic examinations in patients who underwent tethering band resection without osteotomy showed considerable remodeling. Nonunion, multiple surgeries and deformity were the complications in patient who received osteotomy as a part of treatment. Conclusions: The natural history of distal radius FFCD is not clear. Until receiving enough evidences regarding the natural history of this rare lesion, we can recommend the least invasive treatment for the lesion, which is the resection of the fibrous band.

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تاریخ انتشار 2015